Clinical manifestations of prune belly syndrome

Prune Belly Syndrome

Prune belly syndrome is a rare congenital disorder of the urinary system, characterized by a triad of abnormalities. The aetiology is not known. Many infants are either stillborn or die within the first few weeks of life from severe lung or kidney problems, or a combination of congenital anomalies.

Prune Belly Syndrome.

Prune belly syndrome--report of 47 cases.

Forty-seven cases of prune belly syndrome in children born between 1948 and 1977 are described. They have been classified into three groups according to the state of the urinary tract in the neonatal period. The results achieved in these cases form the basis of our present management. In group I, the most severely affected, early death is inevitable. In group 2 the children are ill as neonates;...

Concurrence of prune belly syndrome with meningomyelocele

Prune Belly Syndrome (PBS) comprises a triad of abdominal wall deficiency, urogenital abnormalities and cryptorchidism. Neurologic abnormalities are unusual in prune belly syndrome. Here, we report a rare association of meningomyelocele with prune belly syndrome and provide an embryologic perspective to this concurrence.

Prune Belly Syndrome with Situs Inversus Abdominus

A full term male baby born to a 23-year-old primigravida did not develop spontaneous respiration after birth. His heart rate was <40/min and required bag and tube ventilation; and shifted to NICU for further management. Antenatal ultrasound at 36 weeks showed single live fetus with grossly distended bladder with dilated proximal urethra, bilateral hydroureters causing significant intra-abdomina...